Laparoscopic myomectomy in a patient with laparoscopic vaginoplasty (modified Davydov) and a review of the literature

Mayer-Rokitansky-Kuster-Hauser (MRKH) syndrome is characterized by congenital absence of the uterus and vagina, or uterus may be rudimentary. Coexistence of myoma uteri with MRKH syndrome is possible. The case presented in this study is the 18th report in the literature. Moreover, it is the first with coexistent skeletal system anomalies, left pelvic renal ectopia, and leiomyoma of the rudimentary uterus. Review of English-language medical literature revealed that coexistence of uterine leiomyoma and MRKH syndrome is very rare. However, if a patient with MRKH syndrome presents with a pelvic mass, the possibility of leiomyoma should be considered.