Congenital anomalies of the pancreas are quite common. The cases may present with different symptoms at different ages. While severe forms cause more noisy pictures in infancy and early childhood, mild forms may give symptoms in adulthood or they may be completely asymptomatic. Being aware of these anomalies guides clinicians in terms of diagnosis in clinical approach and helps prevent undesirable complications, especially during biliary, liver, and pancreatic operations. This case report aimed to present a case with annular pancreas and accompanying ectopic pancreas presenting in adult age with complaints consistent with severe upper gastrointestinal system obstruction with clinical, radiological, and endoscopic findings.Keywords: Annular pancreas, congenital pancreatic anomalies; duodenal obstruction; ectopic pancreas; endoscopy.